Comparison of three clinical rating scales in Friedreich ataxia (FRDA)
Identifieur interne : 002383 ( Main/Exploration ); précédent : 002382; suivant : 002384Comparison of three clinical rating scales in Friedreich ataxia (FRDA)
Auteurs : Katrin Bürk [Allemagne] ; Ulrike M Lzig [Allemagne] ; Stefanie Wolf [Allemagne] ; Suzette Heck [Allemagne] ; Konstantinos Dimitriadis [Allemagne] ; Tanja Schmitz-Hübsch [Allemagne] ; Sascha Hering [Autriche] ; Tobias M. Lindig [Allemagne] ; Verena Haug [Allemagne] ; Dagmar Timmann [Allemagne] ; Ingrid Degen [Allemagne] ; Bernd Kruse [Allemagne] ; Jan-Markus Dörr [Allemagne] ; Susanne Ratzka [Allemagne] ; Anja Ivo [Allemagne] ; Ludger Schöls [Allemagne] ; Sylvia Boesch [Autriche] ; Thomas Klockgether [Allemagne] ; Thomas Klopstock [Allemagne] ; Jörg B. Schulz [Allemagne]Source :
- Movement Disorders [ 0885-3185 ] ; 2009-09-15.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
- Adolescent, Adult, Aged, Child, Comparative study, Disability Evaluation, FARS, Female, Friedreich Ataxia (diagnosis), Friedreich Ataxia (genetics), Friedreich Ataxia (physiopathology), Friedreich ataxia, Humans, ICARS, Male, Middle Aged, Nervous system diseases, Outcome Assessment (Health Care), Principal Component Analysis, Psychometrics, Reproducibility of Results, SARA, Severity of Illness Index, Statistics as Topic, Validation, Young Adult, clinical rating scales, validation.
- MESH :
- diagnosis : Friedreich Ataxia.
- genetics : Friedreich Ataxia.
- physiopathology : Friedreich Ataxia.
- Adolescent, Adult, Aged, Child, Disability Evaluation, Female, Humans, Male, Middle Aged, Outcome Assessment (Health Care), Principal Component Analysis, Psychometrics, Reproducibility of Results, Severity of Illness Index, Statistics as Topic, Young Adult.
Abstract
To test the validity and reliability of the scale for the assessment and rating of ataxia (SARA) in Friedreich ataxia (FRDA). SARA is limited to eight items and can be performed rapidly. Ninety‐six patients with a molecular genetic diagnosis of FRDA were rated using three different clinical scales, the FRDA Rating Scale (FARS), the International Cooperative Ataxia Rating Scale (ICARS), and SARA. Despite considerable discrepancies in scale size and subscale structure, SARA total scores were significantly correlated with ICARS (r = 0.953, P < 0.0001) and FARS (r = 0.938, P < 0.0001) total scores. SARA total scores also correlated with the activities of daily living (ADL, r = 0.929, P < 0.0001). Although originally developed for the use in dominantly inherited ataxias, which are primarily ataxias of the cerebellar type, SARA can also be used successfully to assess afferent ataxia, which is the predominant form in FRDA. Because SARA is characterized by high interrater reliability and practicability, SARA is applicable and well suited forclinical trials of FRDA. © 2009 Movement Disorder Society
Url:
DOI: 10.1002/mds.22660
Affiliations:
- Allemagne, Autriche
- Bade-Wurtemberg, Basse-Saxe, Bavière, Berlin, District de Cologne, District de Fribourg-en-Brisgau, District de Giessen, District de Haute-Bavière, District de Tübingen, Hambourg, Hesse (Land), Rhénanie-du-Nord-Westphalie
- Berlin, Bonn, Fribourg-en-Brisgau, Göttingen, Hambourg, Marbourg, Munich, Tübingen
- Université Louis-et-Maximilien de Munich
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Le document en format XML
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Lindig</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurodegeneration and Hertie‐Institute for Clinical Brain Research, University of Tübingen, Tübingen</wicri:regionArea><placeName><region type="land" nuts="1">Bade-Wurtemberg</region><region type="district" nuts="2">District de Tübingen</region><settlement type="city">Tübingen</settlement></placeName></affiliation></author><author><name sortKey="Haug, Verena" sort="Haug, Verena" uniqKey="Haug V" first="Verena" last="Haug">Verena Haug</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neuropediatrics, University of Freiburg, Freiburg</wicri:regionArea><placeName><region type="land" nuts="1">Bade-Wurtemberg</region><region type="district" nuts="2">District de Fribourg-en-Brisgau</region><settlement type="city">Fribourg-en-Brisgau</settlement></placeName></affiliation></author><author><name sortKey="Timmann, Dagmar" sort="Timmann, Dagmar" uniqKey="Timmann D" first="Dagmar" last="Timmann">Dagmar Timmann</name><affiliation wicri:level="1"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurology, University of Essen, Essen</wicri:regionArea><wicri:noRegion>Essen</wicri:noRegion><wicri:noRegion>Essen</wicri:noRegion></affiliation></author><author><name sortKey="Degen, Ingrid" sort="Degen, Ingrid" uniqKey="Degen I" first="Ingrid" last="Degen">Ingrid Degen</name><affiliation wicri:level="1"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neuropediatrics, Sankt Elisabeth Krankenhaus, Neuwied</wicri:regionArea><wicri:noRegion>Neuwied</wicri:noRegion><wicri:noRegion>Neuwied</wicri:noRegion></affiliation></author><author><name sortKey="Kruse, Bernd" sort="Kruse, Bernd" uniqKey="Kruse B" first="Bernd" last="Kruse">Bernd Kruse</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neuropediatrics, University of Hamburg, Hamburg</wicri:regionArea><placeName><settlement type="city">Hambourg</settlement><region type="land" nuts="2">Hambourg</region></placeName></affiliation></author><author><name sortKey="Dorr, Jan Arkus" sort="Dorr, Jan Arkus" uniqKey="Dorr J" first="Jan-Markus" last="Dörr">Jan-Markus Dörr</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurology, Helios‐Klinikum, Berlin</wicri:regionArea><placeName><region type="land" nuts="3">Berlin</region><settlement type="city">Berlin</settlement></placeName></affiliation></author><author><name sortKey="Ratzka, Susanne" sort="Ratzka, Susanne" uniqKey="Ratzka S" first="Susanne" last="Ratzka">Susanne Ratzka</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurodegeneration and Restorative Research, Centers of Molecular Physiology of the Brain and Neurological Medicine, University of Göttingen, Göttingen</wicri:regionArea><placeName><region type="land" nuts="2">Basse-Saxe</region><settlement type="city">Göttingen</settlement></placeName></affiliation></author><author><name sortKey="Ivo, Anja" sort="Ivo, Anja" uniqKey="Ivo A" first="Anja" last="Ivo">Anja Ivo</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurology, University of Bonn, Bonn</wicri:regionArea><placeName><region type="land" nuts="1">Rhénanie-du-Nord-Westphalie</region><region type="district" nuts="2">District de Cologne</region><settlement type="city">Bonn</settlement></placeName></affiliation></author><author><name sortKey="Schols, Ludger" sort="Schols, Ludger" uniqKey="Schols L" first="Ludger" last="Schöls">Ludger Schöls</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurodegeneration and Hertie‐Institute for Clinical Brain Research, University of Tübingen, Tübingen</wicri:regionArea><placeName><region type="land" nuts="1">Bade-Wurtemberg</region><region type="district" nuts="2">District de Tübingen</region><settlement type="city">Tübingen</settlement></placeName></affiliation></author><author><name sortKey="Boesch, Sylvia" sort="Boesch, Sylvia" uniqKey="Boesch S" first="Sylvia" last="Boesch">Sylvia Boesch</name><affiliation wicri:level="1"><country xml:lang="fr">Autriche</country><wicri:regionArea>Department of Neurology, University of Innsbruck, Innsbruck</wicri:regionArea><wicri:noRegion>Innsbruck</wicri:noRegion></affiliation></author><author><name sortKey="Klockgether, Thomas" sort="Klockgether, Thomas" uniqKey="Klockgether T" first="Thomas" last="Klockgether">Thomas Klockgether</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurology, University of Bonn, Bonn</wicri:regionArea><placeName><region type="land" nuts="1">Rhénanie-du-Nord-Westphalie</region><region type="district" nuts="2">District de Cologne</region><settlement type="city">Bonn</settlement></placeName></affiliation></author><author><name sortKey="Klopstock, Thomas" sort="Klopstock, Thomas" uniqKey="Klopstock T" first="Thomas" last="Klopstock">Thomas Klopstock</name><affiliation wicri:level="4"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurology, University of Munich, Munich</wicri:regionArea><placeName><region type="land" nuts="1">Bavière</region><region type="district" nuts="2">District de Haute-Bavière</region><settlement type="city">Munich</settlement></placeName><orgName type="university">Université Louis-et-Maximilien de Munich</orgName></affiliation></author><author><name sortKey="Schulz, Jorg B" sort="Schulz, Jorg B" uniqKey="Schulz J" first="Jörg B." last="Schulz">Jörg B. Schulz</name><affiliation wicri:level="3"><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Neurodegeneration and Restorative Research, Centers of Molecular Physiology of the Brain and Neurological Medicine, University of Göttingen, Göttingen</wicri:regionArea><placeName><region type="land" nuts="2">Basse-Saxe</region><settlement type="city">Göttingen</settlement></placeName></affiliation></author></analytic><monogr></monogr><series><title level="j">Movement Disorders</title><title level="j" type="abbrev">Mov. Disord.</title><idno type="ISSN">0885-3185</idno><idno type="eISSN">1531-8257</idno><imprint><publisher>Wiley Subscription Services, Inc., A Wiley Company</publisher><pubPlace>Hoboken</pubPlace><date type="published" when="2009-09-15">2009-09-15</date><biblScope unit="vol">24</biblScope><biblScope unit="issue">12</biblScope><biblScope unit="page" from="1779">1779</biblScope><biblScope unit="page" to="1784">1784</biblScope></imprint><idno type="ISSN">0885-3185</idno></series><idno type="istex">11716E91D5B8E246E8005900F0EC1220736FD113</idno><idno type="DOI">10.1002/mds.22660</idno><idno type="ArticleID">MDS22660</idno></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0885-3185</idno></seriesStmt></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adolescent</term><term>Adult</term><term>Aged</term><term>Child</term><term>Comparative study</term><term>Disability Evaluation</term><term>FARS</term><term>Female</term><term>Friedreich Ataxia (diagnosis)</term><term>Friedreich Ataxia (genetics)</term><term>Friedreich Ataxia (physiopathology)</term><term>Friedreich ataxia</term><term>Humans</term><term>ICARS</term><term>Male</term><term>Middle Aged</term><term>Nervous system diseases</term><term>Outcome Assessment (Health Care)</term><term>Principal Component Analysis</term><term>Psychometrics</term><term>Reproducibility of Results</term><term>SARA</term><term>Severity of Illness Index</term><term>Statistics as Topic</term><term>Validation</term><term>Young Adult</term><term>clinical rating scales</term><term>validation</term></keywords><keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Friedreich Ataxia</term></keywords><keywords scheme="MESH" qualifier="genetics" xml:lang="en"><term>Friedreich Ataxia</term></keywords><keywords scheme="MESH" qualifier="physiopathology" xml:lang="en"><term>Friedreich Ataxia</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Adolescent</term><term>Adult</term><term>Aged</term><term>Child</term><term>Disability Evaluation</term><term>Female</term><term>Humans</term><term>Male</term><term>Middle Aged</term><term>Outcome Assessment (Health Care)</term><term>Principal Component Analysis</term><term>Psychometrics</term><term>Reproducibility of Results</term><term>Severity of Illness Index</term><term>Statistics as Topic</term><term>Young Adult</term></keywords><keywords scheme="Pascal" xml:lang="fr"><term>Etude comparative</term><term>Hérédodégénérescence spinocérébelleuse de Friedreich</term><term>Pathologie du système nerveux</term><term>Validation</term></keywords></textClass><langUsage><language ident="en">en</language></langUsage></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">To test the validity and reliability of the scale for the assessment and rating of ataxia (SARA) in Friedreich ataxia (FRDA). SARA is limited to eight items and can be performed rapidly. Ninety‐six patients with a molecular genetic diagnosis of FRDA were rated using three different clinical scales, the FRDA Rating Scale (FARS), the International Cooperative Ataxia Rating Scale (ICARS), and SARA. Despite considerable discrepancies in scale size and subscale structure, SARA total scores were significantly correlated with ICARS (r = 0.953, P < 0.0001) and FARS (r = 0.938, P < 0.0001) total scores. SARA total scores also correlated with the activities of daily living (ADL, r = 0.929, P < 0.0001). Although originally developed for the use in dominantly inherited ataxias, which are primarily ataxias of the cerebellar type, SARA can also be used successfully to assess afferent ataxia, which is the predominant form in FRDA. Because SARA is characterized by high interrater reliability and practicability, SARA is applicable and well suited forclinical trials of FRDA. © 2009 Movement Disorder Society</div></front></TEI><affiliations><list><country><li>Allemagne</li><li>Autriche</li></country><region><li>Bade-Wurtemberg</li><li>Basse-Saxe</li><li>Bavière</li><li>Berlin</li><li>District de Cologne</li><li>District de Fribourg-en-Brisgau</li><li>District de Giessen</li><li>District de Haute-Bavière</li><li>District de Tübingen</li><li>Hambourg</li><li>Hesse (Land)</li><li>Rhénanie-du-Nord-Westphalie</li></region><settlement><li>Berlin</li><li>Bonn</li><li>Fribourg-en-Brisgau</li><li>Göttingen</li><li>Hambourg</li><li>Marbourg</li><li>Munich</li><li>Tübingen</li></settlement><orgName><li>Université Louis-et-Maximilien de Munich</li></orgName></list><tree><country name="Allemagne"><region name="Basse-Saxe"><name sortKey="Burk, Katrin" sort="Burk, Katrin" uniqKey="Burk K" first="Katrin" last="Bürk">Katrin Bürk</name></region><name sortKey="Burk, Katrin" sort="Burk, Katrin" uniqKey="Burk K" first="Katrin" last="Bürk">Katrin Bürk</name><name sortKey="Degen, Ingrid" sort="Degen, Ingrid" uniqKey="Degen I" first="Ingrid" last="Degen">Ingrid Degen</name><name sortKey="Dimitriadis, Konstantinos" sort="Dimitriadis, Konstantinos" uniqKey="Dimitriadis K" first="Konstantinos" last="Dimitriadis">Konstantinos Dimitriadis</name><name sortKey="Dorr, Jan Arkus" sort="Dorr, Jan Arkus" uniqKey="Dorr J" first="Jan-Markus" last="Dörr">Jan-Markus Dörr</name><name sortKey="Haug, Verena" sort="Haug, Verena" uniqKey="Haug V" first="Verena" last="Haug">Verena Haug</name><name sortKey="Heck, Suzette" sort="Heck, Suzette" uniqKey="Heck S" first="Suzette" last="Heck">Suzette Heck</name><name sortKey="Ivo, Anja" sort="Ivo, Anja" uniqKey="Ivo A" first="Anja" last="Ivo">Anja Ivo</name><name sortKey="Klockgether, Thomas" sort="Klockgether, Thomas" uniqKey="Klockgether T" first="Thomas" last="Klockgether">Thomas Klockgether</name><name sortKey="Klopstock, Thomas" sort="Klopstock, Thomas" uniqKey="Klopstock T" first="Thomas" last="Klopstock">Thomas Klopstock</name><name sortKey="Kruse, Bernd" sort="Kruse, Bernd" uniqKey="Kruse B" first="Bernd" last="Kruse">Bernd Kruse</name><name sortKey="Lindig, Tobias M" sort="Lindig, Tobias M" uniqKey="Lindig T" first="Tobias M." last="Lindig">Tobias M. Lindig</name><name sortKey="M Lzig, Ulrike" sort="M Lzig, Ulrike" uniqKey="M Lzig U" first="Ulrike" last="M Lzig">Ulrike M Lzig</name><name sortKey="Ratzka, Susanne" sort="Ratzka, Susanne" uniqKey="Ratzka S" first="Susanne" last="Ratzka">Susanne Ratzka</name><name sortKey="Schmitz Bsch, Tanja" sort="Schmitz Bsch, Tanja" uniqKey="Schmitz Bsch T" first="Tanja" last="Schmitz-Hübsch">Tanja Schmitz-Hübsch</name><name sortKey="Schols, Ludger" sort="Schols, Ludger" uniqKey="Schols L" first="Ludger" last="Schöls">Ludger Schöls</name><name sortKey="Schulz, Jorg B" sort="Schulz, Jorg B" uniqKey="Schulz J" first="Jörg B." last="Schulz">Jörg B. Schulz</name><name sortKey="Timmann, Dagmar" sort="Timmann, Dagmar" uniqKey="Timmann D" first="Dagmar" last="Timmann">Dagmar Timmann</name><name sortKey="Wolf, Stefanie" sort="Wolf, Stefanie" uniqKey="Wolf S" first="Stefanie" last="Wolf">Stefanie Wolf</name></country><country name="Autriche"><noRegion><name sortKey="Hering, Sascha" sort="Hering, Sascha" uniqKey="Hering S" first="Sascha" last="Hering">Sascha Hering</name></noRegion><name sortKey="Boesch, Sylvia" sort="Boesch, Sylvia" uniqKey="Boesch S" first="Sylvia" last="Boesch">Sylvia Boesch</name></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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